What is Phenylketonuria (PKU)?
Amino acids - phenylalanine
The ‘building blocks’ of protein are called amino acids. In PKU, due to the lack of an enzyme, the body cannot properly deal with one of the amino acids, phenylalanine. People with PKU therefore need to severely restrict the amount of protein they eat.
Protein substitutes for PKU
A key element in the management of PKU is the use of protein substitutes. Protein substitutes for PKU provide all the amino acids found in protein but no phenylalanine. In combination with the small allowance of regular dietary protein, protein substitutes ensure that an individual with PKU has an adequate intake of protein.
Vitaflo produces a range of age-specific, lifestyle-friendly and palatable protein substitutes for PKU.
Our product range for PKU
Our support product range
Our healthcare professional resources for PKU
PKU Sphere Guidelines
The introduction and use of PKU sphere™, a Glycomacropeptide (GMP) based protein substitute, in children and adults with PKU.A clinical resource for healthcare professionals wishing to learn more about GMP, its potential benefits and how to successfully introduce PKU sphere in children and adults.
PKU Gel Guidelines
The introduction of complementary foods & transitioning to a second stage protein substitute (PKU gel™) in infants.A clinical resource for healthcare professionals wishing to learn more about weaning an infant with PKU, how to introduce PKU gel and practical points and troubleshooting when using PKU gel.
PKU case studies
STARTING SOLIDS AND INTRODUCING A SECOND STAGE PROTEIN SUBSTITUTE (PKU GEL™)
Prof. Anita MacDonald, Consultant Dietitian in Inherited Metabolic Disorders, Birmingham Children’s Hospital
USE OF PKU SPHERE AS A PROTEIN SUBSTITUTE DURING PRECONCEPTION FOR A PATIENT WITH HYPERPHENYLALANINEMIA
Melanie Hill, Specialist Dietitian for Adults with Inherited Metabolic Diseases, Sheffield Teaching Hospitals NHS Foundation Trust
Online resource for PKU patients
AN ONLINE RESOURCE TO SUPPORT PATIENTS AND THEIR FAMILIES AT EVERY STAGE OF THEIR VITAFRIENDS PKU PRODUCT JOURNEY.
At VitafriendsPKU patients will find all the information they need to know about their protein substitute: how to make and take it, available flavours and what products their healthcare professional may talk to them about. There are also helpful hints and a wide range of recipes to support patients on their PKU diet.
Inborn Errors of Metabolism
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