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Creatine

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Product Range Creatine5000
Pack Size 30 x 6g ℮
Ingredients Creatine monohydrate, Maltodextrin, Thickener (E415).


Description
Indication

Clinical Use


Cerebral creatine deficiency syndrome (CCDS)1


CCDS is a group of inborn errors of L-creatine metabolism. Individuals with these disorders experience global developmental delay, intellectual disability and associated behavioural and neurological manifestations such as seizures, movement disorders and myopathy.


Within CCDS, there are two disorders of L-creatine biosynthesis; guanidinoacetate methyltransferase (GAMT) deficiency and L-arginine:glycine amidinotransferase (AGAT) deficiency. The diet is supplemented with oral creatine monohydrate to replenish L-creatine levels in the brain and other tissues in individuals with GAMT and AGAT.



Preparation Guidelines


To be determined by the clinician or dietitian. Suggested methods include:


1. Measure out 50ml of water into a shaker.
2. Add one sachet.
3. SHAKE vigorously for 30 seconds and serve. Water or permitted drinks should be consumed after Creatine5000.




Webinar

1. Pour the liquid protein substitute into a shaker.
2. Add in the SDAA.
3. Shake for 30 seconds.
4. Serve.




1. Mix the dry SDAA and protein substitute powders together.
2. Follow the protein substitute preparation instructions. You may wish to use extra water.
3. Serve.




Further Reading


1. Cerebral Creatine Deficiency Syndromes. https://rarediseases.org/rare-diseases/cerebral-creatine-deficiency-syndromes/#:~:text=Cerebral%20creatine%20deficiency%20syndromes%20(CCDS,all%20cells%20in%20the%20body. Accessed March 2022.


Creatine5000 is a Food for Special Medical Purposes for the dietary management of inborn errors of metabolism. For use under medical supervision. For healthcare professional use only.